FY2026
Effective from
- Added
Disorders of pyrophosphate metabolism
Category — select a more specific code
CDC/NCHS · FY2026Ehlers-Danlos syndromes (Q79.6-)
For US diagnosis claims covered by HIPAA, ICD-10-CM is required from October 1, 2015.
Use the service date for outpatient/professional claims and the discharge date for hospital inpatient claims. Earlier encounters use ICD-9-CM; each individual code must also be valid for the applicable date.
Official coding guidelines → · CMS ↗First observed · 2025-10-01
Latest recorded change · FY2026
Effective from
Disorders of pyrophosphate metabolism
Category — select a more specific code
CDC/NCHS · FY2026| All editions | Effective from | Code history |
|---|---|---|
| FY2026 | 2025-10-01 | Added |
| FY2026 · April | 2026-04-01 | No tabular change |
| FY2027 | 2026-10-01 | No tabular change |
The official Tabular List has no additional instructions at this code level.
Review the instructions inherited from its parent categories below. Inherited instructions ↓
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Ehlers-Danlos syndromes (Q79.6-)
E83.820Generalized arterial calcification of infancy with unspecified genetic causalityBillable / specificE83.821ENPP1 deficiency causing generalized arterial calcification of infancyBillable / specificE83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2Billable / specificE83.823ABCC6 deficiency causing generalized arterial calcification of infancyBillable / specificE83.824ABCC6 deficiency causing pseudoxanthoma elasticumBillable / specificE83.825CD73 deficiency causing arterial calcificationBillable / specificOther entries in the same category; these are not automatic substitutes.
| Code | Description | Category · further specificity required |
|---|---|---|
| E83.81 | Hungry bone syndrome | Billable / specific |
| E83.89 | Other disorders of mineral metabolism | Billable / specific |
Official titles and instructions are preserved in their source language. Official sources ↗
Excludes 2 · disorders of pyrophosphate metabolism (E83.82-)
Excludes 2 · disorders of pyrophosphate metabolism (E83.82-)
Excludes 2 · disorders of pyrophosphate metabolism (E83.82-)
Excludes 2 · disorders of pyrophosphate metabolism (E83.82-)