FY2024
Effective from
- Inherited rules changed
Other sphingolipidosis
Category — select a more specific code
CDC/NCHS · FY2024adrenoleukodystrophy [Addison-Schilder] (E71.528)
Ehlers-Danlos syndromes (Q79.6-)
For US diagnosis claims covered by HIPAA, ICD-10-CM is required from October 1, 2015.
Use the service date for outpatient/professional claims and the discharge date for hospital inpatient claims. Earlier encounters use ICD-9-CM; each individual code must also be valid for the applicable date.
Official coding guidelines → · CMS ↗First observed · 2015-10-01
Latest recorded change · FY2024
Effective from
Other sphingolipidosis
Category — select a more specific code
CDC/NCHS · FY2024| All editions | Effective from | Code history |
|---|---|---|
| FY2016 | 2015-10-01 | First observed |
| FY2017 | 2016-10-01 | No tabular change |
| FY2018 | 2017-10-01 | No tabular change |
| FY2019 | 2018-10-01 | No tabular change |
| FY2020 | 2019-10-01 | Inherited rules changed |
| FY2020 · April | 2020-04-01 | No tabular change |
| FY2021 | 2020-10-01 | Inherited rules changed |
| FY2021 · 01-01 | 2021-01-01 | No tabular change |
| FY2022 | 2021-10-01 | Inherited rules changed |
| FY2022 · 04-01 | 2022-04-01 | No tabular change |
| FY2023 | 2022-10-01 | No tabular change |
| FY2023 · 04-01 | 2023-04-01 | No tabular change |
| FY2024 | 2023-10-01 | Inherited rules changed |
| FY2024 · 04-01 | 2024-04-01 | No tabular change |
| FY2025 | 2024-10-01 | No tabular change |
| FY2025 · 04-01 | 2025-04-01 | No tabular change |
| FY2026 | 2025-10-01 | No tabular change |
| FY2026 · April | 2026-04-01 | No tabular change |
| FY2027 | 2026-10-01 | No tabular change |
adrenoleukodystrophy [Addison-Schilder] (E71.528)
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Ehlers-Danlos syndromes (Q79.6-)
E75.21Fabry (-Anderson) diseaseBillable / specificE75.22Gaucher diseaseBillable / specificE75.23Krabbe diseaseBillable / specificE75.24Niemann-Pick diseaseCategory · further specificity requiredE75.25Metachromatic leukodystrophyBillable / specificE75.26Sulfatase deficiencyBillable / specificE75.27Pelizaeus-Merzbacher diseaseBillable / specificE75.28Canavan diseaseBillable / specificE75.29Other sphingolipidosisBillable / specificOther entries in the same category; these are not automatic substitutes.
| Code | Description | Category · further specificity required |
|---|---|---|
| E75.0 | GM2 gangliosidosis | Category · further specificity required |
| E75.1 | Other and unspecified gangliosidosis | Category · further specificity required |
| E75.3 | Sphingolipidosis, unspecified | Billable / specific |
| E75.4 | Neuronal ceroid lipofuscinosis | Billable / specific |
| E75.5 | Other lipid storage disorders | Billable / specific |
| E75.6 | Lipid storage disorder, unspecified | Billable / specific |
Official titles and instructions are preserved in their source language. Official sources ↗