Effective from
- Inherited rules changed
Disorders of fatty-acid oxidation
Category — select a more specific code
CDC/NCHS · FY2024Ehlers-Danlos syndromes (Q79.6-)
carnitine deficiency due to inborn error of metabolism (E71.42)
For US diagnosis claims covered by HIPAA, ICD-10-CM is required from October 1, 2015.
Use the service date for outpatient/professional claims and the discharge date for hospital inpatient claims. Earlier encounters use ICD-9-CM; each individual code must also be valid for the applicable date.
Official coding guidelines → · CMS ↗First observed · 2015-10-01
Latest recorded change · FY2024
Effective from
Disorders of fatty-acid oxidation
Category — select a more specific code
CDC/NCHS · FY2024| All editions | Effective from | Code history |
|---|---|---|
| FY2016 | 2015-10-01 | First observed |
| FY2017 | 2016-10-01 | No tabular change |
| FY2018 | 2017-10-01 | No tabular change |
| FY2019 | 2018-10-01 | No tabular change |
| FY2020 | 2019-10-01 | Inherited rules changed |
| FY2020 · April | 2020-04-01 | No tabular change |
| FY2021 | 2020-10-01 | Inherited rules changed |
| FY2021 · 01-01 | 2021-01-01 | No tabular change |
| FY2022 | 2021-10-01 | Inherited rules changed |
| FY2022 · 04-01 | 2022-04-01 | No tabular change |
| FY2023 | 2022-10-01 | No tabular change |
| FY2023 · 04-01 | 2023-04-01 | No tabular change |
| FY2024 | 2023-10-01 | Inherited rules changed |
| FY2024 · 04-01 | 2024-04-01 | No tabular change |
| FY2025 | 2024-10-01 | No tabular change |
| FY2025 · 04-01 | 2025-04-01 | No tabular change |
| FY2026 | 2025-10-01 | No tabular change |
| FY2026 · April | 2026-04-01 | No tabular change |
| FY2027 | 2026-10-01 | No tabular change |
The official Tabular List has no additional instructions at this code level.
Review the instructions inherited from its parent categories below. Inherited instructions ↓
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Ehlers-Danlos syndromes (Q79.6-)
carnitine deficiency due to inborn error of metabolism (E71.42)
E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillable / specificE71.311Medium chain acyl CoA dehydrogenase deficiencyBillable / specificE71.312Short chain acyl CoA dehydrogenase deficiencyBillable / specificE71.313Glutaric aciduria type IIBillable / specificE71.314Muscle carnitine palmitoyltransferase deficiencyBillable / specificE71.318Other disorders of fatty-acid oxidationBillable / specificOther entries in the same category; these are not automatic substitutes.
| Code | Description | Category · further specificity required |
|---|---|---|
| E71.30 | Disorder of fatty-acid metabolism, unspecified | Billable / specific |
| E71.32 | Disorders of ketone metabolism | Billable / specific |
| E71.39 | Other disorders of fatty-acid metabolism | Billable / specific |
Official titles and instructions are preserved in their source language. Official sources ↗