FY2026
Effective from
- Added
ENPP1 deficiency causing generalized arterial calcification of infancy
Billable diagnosis code
CDC/NCHS · FY2026Ehlers-Danlos syndromes (Q79.6-)
Coverage depends on the payer, service and applicable policy. A billable code does not guarantee payment.
For US diagnosis claims covered by HIPAA, ICD-10-CM is required from October 1, 2015.
Use the service date for outpatient/professional claims and the discharge date for hospital inpatient claims. Earlier encounters use ICD-9-CM; each individual code must also be valid for the applicable date.
Official coding guidelines → · CMS ↗Grouping depends on the complete encounter and CMS grouper logic.
2026-04-01 – 2026-09-30
CMS · MS-DRG 43.1First observed · 2025-10-01
Latest recorded change · FY2026
Effective from
ENPP1 deficiency causing generalized arterial calcification of infancy
Billable diagnosis code
CDC/NCHS · FY2026| All editions | Effective from | Code history |
|---|---|---|
| FY2026 | 2025-10-01 | Added |
| FY2026 · April | 2026-04-01 | No tabular change |
| FY2027 | 2026-10-01 | No tabular change |
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Ehlers-Danlos syndromes (Q79.6-)
Historical assignments from the CDC conversion table support data retrieval. They do not authorize substituting a previous code for the current code.
Previous assignment: E83.89
Other entries in the same category; these are not automatic substitutes.
| Code | Description | Category · further specificity required |
|---|---|---|
| E83.820 | Generalized arterial calcification of infancy with unspecified genetic causality | Billable / specific |
| E83.822 | ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2 | Billable / specific |
| E83.823 | ABCC6 deficiency causing generalized arterial calcification of infancy | Billable / specific |
| E83.824 | ABCC6 deficiency causing pseudoxanthoma elasticum | Billable / specific |
| E83.825 | CD73 deficiency causing arterial calcification | Billable / specific |
Official titles and instructions are preserved in their source language. Official sources ↗