FY2024
Effective from
- Inherited rules changed
Niemann-Pick disease
Category — select a more specific code
CDC/NCHS · FY2024adrenoleukodystrophy [Addison-Schilder] (E71.528)
Ehlers-Danlos syndromes (Q79.6-)
For US diagnosis claims covered by HIPAA, ICD-10-CM is required from October 1, 2015.
Use the service date for outpatient/professional claims and the discharge date for hospital inpatient claims. Earlier encounters use ICD-9-CM; each individual code must also be valid for the applicable date.
Official coding guidelines → · CMS ↗First observed · 2015-10-01
Latest recorded change · FY2024
Effective from
Niemann-Pick disease
Category — select a more specific code
CDC/NCHS · FY2024| All editions | Effective from | Code history |
|---|---|---|
| FY2016 | 2015-10-01 | First observed |
| FY2017 | 2016-10-01 | No tabular change |
| FY2018 | 2017-10-01 | No tabular change |
| FY2019 | 2018-10-01 | No tabular change |
| FY2020 | 2019-10-01 | Inherited rules changed |
| FY2020 · April | 2020-04-01 | No tabular change |
| FY2021 | 2020-10-01 | Inherited rules changed |
| FY2021 · 01-01 | 2021-01-01 | No tabular change |
| FY2022 | 2021-10-01 | Code-level rules changed · Inherited rules changed |
| FY2022 · 04-01 | 2022-04-01 | No tabular change |
| FY2023 | 2022-10-01 | No tabular change |
| FY2023 · 04-01 | 2023-04-01 | No tabular change |
| FY2024 | 2023-10-01 | Inherited rules changed |
| FY2024 · 04-01 | 2024-04-01 | No tabular change |
| FY2025 | 2024-10-01 | No tabular change |
| FY2025 · 04-01 | 2025-04-01 | No tabular change |
| FY2026 | 2025-10-01 | No tabular change |
| FY2026 · April | 2026-04-01 | No tabular change |
| FY2027 | 2026-10-01 | No tabular change |
Acid sphingomyelinase deficiency (ASMD)
All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Ehlers-Danlos syndromes (Q79.6-)
adrenoleukodystrophy [Addison-Schilder] (E71.528)
E75.240Niemann-Pick disease type ABillable / specificE75.241Niemann-Pick disease type BBillable / specificE75.242Niemann-Pick disease type CBillable / specificE75.243Niemann-Pick disease type DBillable / specificE75.244Niemann-Pick disease type A/BBillable / specificE75.248Other Niemann-Pick diseaseBillable / specificE75.249Niemann-Pick disease, unspecifiedBillable / specificOther entries in the same category; these are not automatic substitutes.
| Code | Description | Category · further specificity required |
|---|---|---|
| E75.21 | Fabry (-Anderson) disease | Billable / specific |
| E75.22 | Gaucher disease | Billable / specific |
| E75.23 | Krabbe disease | Billable / specific |
| E75.25 | Metachromatic leukodystrophy | Billable / specific |
| E75.26 | Sulfatase deficiency | Billable / specific |
| E75.27 | Pelizaeus-Merzbacher disease | Billable / specific |
| E75.28 | Canavan disease | Billable / specific |
| E75.29 | Other sphingolipidosis | Billable / specific |
Official titles and instructions are preserved in their source language. Official sources ↗