World Health Organization · 2026-01 · English
4A01.0 Immunodeficiencies with predominantly antibody defects
Official WHO ICD-11 MMS tabulation. This international classification is separate from US ICD-10-CM. For complete instructions and postcoordination, consult the WHO browser.
More specific codes
4A01.00Hereditary agammaglobulinaemia with profoundly reduced or absent B cells4A01.01Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells4A01.02Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells4A01.03Transient hypogammaglobulinaemia of infancy4A01.04Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells4A01.05Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells4A01.0YOther specified immunodeficiencies with predominantly antibody defects4A01.0ZImmunodeficiencies with predominantly antibody defects, unspecified© World Health Organization · CC BY-ND 3.0 IGO