World Health Organization · 2026-01 · English
8A03.1 Hereditary ataxia
Official WHO ICD-11 MMS tabulation. This international classification is separate from US ICD-10-CM. For complete instructions and postcoordination, consult the WHO browser.
More specific codes
8A03.10Friedreich ataxia8A03.11Ataxia due to Cerebrotendinous xanthomatosis8A03.12Ataxia due to Refsum disease8A03.13Ataxia due to abetalipoproteinemia8A03.14Hereditary episodic ataxia8A03.15Ataxia due to mitochondrial mutations8A03.16Spinocerebellar ataxia8A03.1YOther specified hereditary ataxia8A03.1ZHereditary ataxia, unspecified© World Health Organization · CC BY-ND 3.0 IGO