World Health Organization · 2026-01 · English
4A00.1 Defects in the complement system
Official WHO ICD-11 MMS tabulation. This international classification is separate from US ICD-10-CM. For complete instructions and postcoordination, consult the WHO browser.
More specific codes
4A00.10Immunodeficiency with an early component of complement deficiency4A00.11Immunodeficiency with a late component of complement deficiency4A00.12Immunodeficiency with factor B deficiency4A00.13Immunodeficiency with factor D anomaly4A00.14Hereditary angioedema4A00.15Acquired angioedema4A00.1YOther specified defects in the complement system4A00.1ZDefects in the complement system, unspecified© World Health Organization · CC BY-ND 3.0 IGO