World Health Organization · 2026-01 · English
Respiratory diseases principally affecting the lung interstitium
Official WHO ICD-11 MMS tabulation. This international classification is separate from US ICD-10-CM. For complete instructions and postcoordination, consult the WHO browser.
More specific codes
CB00Acute respiratory distress syndromeCB01Pulmonary oedemaCB02Pulmonary eosinophiliaCB03Idiopathic interstitial pneumonitisCB04Primary interstitial lung diseases specific to infancy or childhoodCB05Interstitial lung diseases associated with systemic diseasesCB06Pulmonary alveolar microlithiasisCB07LymphangioleiomyomatosisCB0YOther specified respiratory diseases principally affecting the lung interstitiumCB0ZRespiratory diseases principally affecting the lung interstitium, unspecified© World Health Organization · CC BY-ND 3.0 IGO