Bevorstehend01.10.2026 – 30.09.2027
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Krankheitsverzeichnis

Mucopolysaccharidosis

Krankheitsverzeichnis · Modifikatoren und Verweise

Modifikatoren und Verweise · icd10cm-index-2027.xml

Mucopolysaccharidosis

E76.3

Mucopolysaccharidosis

beta-gluduronidase deficiency

E76.29

Mucopolysaccharidosis

cardiopathy

E76.3

Manifestation: I52

Mucopolysaccharidosis

Hunter's syndrome

E76.1

Mucopolysaccharidosis

Hurler's syndrome

E76.01

Mucopolysaccharidosis

Hurler-Scheie syndrome

E76.02

Mucopolysaccharidosis

Maroteaux-Lamy syndrome

E76.29

Mucopolysaccharidosis

Morquio syndrome

E76.219

Mucopolysaccharidosis › Morquio syndrome

A

E76.210

Mucopolysaccharidosis › Morquio syndrome

B

E76.211

Mucopolysaccharidosis › Morquio syndrome

classic

E76.210

Mucopolysaccharidosis

Sanfilippo syndrome

E76.22

Mucopolysaccharidosis

Scheie's syndrome

E76.03

Mucopolysaccharidosis

specified NEC

E76.29

Mucopolysaccharidosis

type

Mucopolysaccharidosis › type

I

Mucopolysaccharidosis › type › I

Hurler's syndrome

E76.01

Mucopolysaccharidosis › type › I

Hurler-Scheie syndrome

E76.02

Mucopolysaccharidosis › type › I

Scheie's syndrome

E76.03

Mucopolysaccharidosis › type

II

E76.1

Mucopolysaccharidosis › type

III

E76.22

Mucopolysaccharidosis › type

IV

E76.219

Mucopolysaccharidosis › type

IVA

E76.210

Mucopolysaccharidosis › type

IVB

E76.211

Mucopolysaccharidosis › type

VI

E76.29

Mucopolysaccharidosis › type

VII

E76.29