Bevorstehend01.10.2026 – 30.09.2027
Referenzwerkzeuge
KrankheitsverzeichnisDeficiency, deficient
Krankheitsverzeichnis · Modifikatoren und Verweise
Modifikatoren und Verweise · icd10cm-index-2027.xml
Deficiency, deficient
Deficiency, deficient3-beta hydroxysteroid dehydrogenase
E25.0
Deficiency, deficient5-alpha reductase(with male pseudohermaphroditism)
E29.1
Deficiency, deficient11-hydroxylase
E25.0
Deficiency, deficient21-hydroxylase
E25.0
Deficiency, deficientAADC(aromatic L-amino acid decarboxylase)
E70.81
Deficiency, deficientABCC6
Deficiency, deficient › ABCC6causing generalized arterial calcification of infancy
E83.823
Deficiency, deficient › ABCC6pseudoxanthoma elasticum
E83.824
Deficiency, deficientabdominal muscle syndrome
Q79.4
Deficiency, deficientaccelerator globulin(Ac G) (blood)
D68.2
Deficiency, deficientAC globulin(congenital) (hereditary)
D68.2
Deficiency, deficient › AC globulin(congenital) (hereditary)acquired
D68.4
Deficiency, deficientacid phosphatase
E83.39
Deficiency, deficientacid sphingomyelinase(ASMD)
E75.249
Deficiency, deficient › acid sphingomyelinase(ASMD)type
Deficiency, deficient › acid sphingomyelinase(ASMD) › typeA
E75.240
Deficiency, deficient › acid sphingomyelinase(ASMD) › typeA/B
E75.244
Deficiency, deficient › acid sphingomyelinase(ASMD) › typeB
E75.241
Deficiency, deficientactivating factor(blood)
D68.2
Deficiency, deficientADA2(adenosine deaminase 2)
D81.32
Deficiency, deficientadenosine deaminase(ADA)
D81.30
Deficiency, deficient › adenosine deaminase(ADA)with severe combined immunodeficiency(SCID)
D81.31
Deficiency, deficient › adenosine deaminase(ADA)partial(type 1)
D81.39
Deficiency, deficient › adenosine deaminase(ADA)specified NEC
D81.39
Deficiency, deficient › adenosine deaminase(ADA)type 1(without SCID) (without severe combined immunodeficiency)
D81.39
Deficiency, deficient › adenosine deaminase(ADA)type 2
D81.32
Deficiency, deficientaldolase(hereditary)
E74.19
Deficiency, deficientalpha-1-antitrypsin
E88.01
Deficiency, deficientamino-acids
E72.9
Deficiency, deficientanemia
See: Anemia
Deficiency, deficientaneurin
E51.9
Deficiency, deficientantibody with
Deficiency, deficient › antibody withhyperimmunoglobulinemia
D80.6
Deficiency, deficient › antibody withnear-normal immunoglobins
D80.6
Deficiency, deficientantidiuretic hormone
E23.2
Deficiency, deficientanti-hemophilic
Deficiency, deficient › anti-hemophilicfactor(A)
D66
Deficiency, deficient › anti-hemophilic › factor(A)B
D67
Deficiency, deficient › anti-hemophilic › factor(A)C
D68.1
Deficiency, deficient › anti-hemophilicglobulin(AHG) NEC
D66
Deficiency, deficientantithrombin(antithrombin III)
D68.59
Deficiency, deficientaromatic L-amino acid decarboxylase(AADC)
E70.81
Deficiency, deficientascorbic acid
E54
Deficiency, deficientattention(disorder) (syndrome)
F98.8
Deficiency, deficient › attention(disorder) (syndrome)with hyperactivity
See: Disorder, attention-deficit hyperactivity
Deficiency, deficientautoprothrombin
Deficiency, deficient › autoprothrombinI
D68.2
Deficiency, deficient › autoprothrombinII
D67
Deficiency, deficient › autoprothrombinC
D68.2
Deficiency, deficientbeta-glucuronidase
E76.29
Deficiency, deficientbiotin
E53.8
Deficiency, deficientbiotin-dependent carboxylase
D81.819
Deficiency, deficientbiotinidase
D81.810
Deficiency, deficientbrancher enzyme(amylopectinosis)
E74.03
Deficiency, deficientcalciferol
E55.9
Deficiency, deficient › calciferolwith
Deficiency, deficient › calciferol › withadult osteomalacia
M83.8
Deficiency, deficient › calciferol › withrickets
See: Rickets
Deficiency, deficientcalcium(dietary)
E58
Deficiency, deficientcalorie, severe
E43
Deficiency, deficient › calorie, severewith marasmus
E41
Deficiency, deficient › calorie, severe › with marasmusand kwashiorkor
E42
Deficiency, deficientcardiac
See: Insufficiency, myocardial
Deficiency, deficientcarnitine
E71.40
Deficiency, deficient › carnitinedue to
Deficiency, deficient › carnitine › due tohemodialysis
E71.43
Deficiency, deficient › carnitine › due toinborn errors of metabolism
E71.42
Deficiency, deficient › carnitine › due toValproic acid therapy
E71.43
Deficiency, deficient › carnitineiatrogenic
E71.43
Deficiency, deficient › carnitinemuscle palmityltransferase
E71.314
Deficiency, deficient › carnitineprimary
E71.41
Deficiency, deficient › carnitinesecondary
E71.448
Deficiency, deficientcarotene
E50.9
Deficiency, deficientCD73 deficiency causing arterial calcification
E83.825
Deficiency, deficientcentral nervous system
G96.89
Deficiency, deficientceruloplasmin(Wilson)
E83.01
Deficiency, deficientcholine
E53.8
Deficiency, deficientChristmas factor
D67
Deficiency, deficientchromium
E61.4
Deficiency, deficientchronic neurovisceral acid sphingomyelinase
E75.244
Deficiency, deficientchronic visceral acid sphingomyelinase
E75.241
Deficiency, deficientclotting(blood)
D68.9
See also: Deficiency, coagulation factor
Deficiency, deficientclotting factor NEC(hereditary)
D68.2
See also: Deficiency, factor
Deficiency, deficientcoagulation NOS
D68.9
Deficiency, deficient › coagulation NOSwith
Deficiency, deficient › coagulation NOS › withectopic pregnancy
O08.1
Deficiency, deficient › coagulation NOS › withmolar pregnancy
O08.1
Deficiency, deficient › coagulation NOSacquired(any)
D68.4
Deficiency, deficient › coagulation NOSantepartum hemorrhage
See: Hemorrhage, antepartum, with coagulation defect
Deficiency, deficient › coagulation NOSclotting factor NEC
D68.2
See also: Deficiency, factor
Deficiency, deficient › coagulation NOSdue to
Deficiency, deficient › coagulation NOS › due tohyperprothrombinemia
D68.4
Deficiency, deficient › coagulation NOS › due toliver disease
D68.4
Deficiency, deficient › coagulation NOS › due tovitamin K deficiency
D68.4
Deficiency, deficient › coagulation NOSnewborn, transient
P61.6
Deficiency, deficient › coagulation NOSpostpartum
O72.3
Deficiency, deficient › coagulation NOSspecified NEC
D68.8
Deficiency, deficientcognitive
F09
Deficiency, deficientcolor vision
H53.50
Deficiency, deficient › color visionachromatopsia
H53.51
Deficiency, deficient › color visionacquired
H53.52
Deficiency, deficient › color visiondeuteranomaly
H53.53
Deficiency, deficient › color visionprotanomaly
H53.54
Deficiency, deficient › color visionspecified type NEC
H53.59
Deficiency, deficient › color visiontritanomaly
H53.55
Deficiency, deficientcombined glucocorticoid and mineralocorticoid
E27.49
Deficiency, deficientcontact factor
D68.2
Deficiency, deficientcopper(nutritional)
E61.0
Deficiency, deficientcorticoadrenal
E27.40
Deficiency, deficient › corticoadrenalprimary
E27.1
Deficiency, deficientcraniofacial axis
Q75.009
Deficiency, deficientcyanocobalamin
E53.8
Deficiency, deficientC1 esterase inhibitor(C1-INH)
D84.1
Deficiency, deficientdebrancher enzyme(limit dextrinosis)
E74.03
Deficiency, deficientdehydrogenase
Deficiency, deficient › dehydrogenaselong chain/very long chain acyl CoA
E71.310
Deficiency, deficient › dehydrogenasemedium chain acyl CoA
E71.311
Deficiency, deficient › dehydrogenaseshort chain acyl CoA
E71.312
Deficiency, deficientdiet
E63.9
Deficiency, deficientdihydropyrimidine dehydrogenase(DPD)
E88.89
Deficiency, deficientdisaccharidase
E73.9
Deficiency, deficientedema
See: Malnutrition, severe
Deficiency, deficientendocrine
E34.9
Deficiency, deficientenergy-supply
See: Malnutrition
Deficiency, deficientENPP1
Deficiency, deficient › ENPP1causing
Deficiency, deficient › ENPP1 › causingautosomal recessive hypophosphatemic rickets type 2
E83.822
Deficiency, deficient › ENPP1 › causinggeneralized arterial calcification of infancy
E83.821
Deficiency, deficientenzymes, circulating NEC
E88.09
Deficiency, deficientergosterol
E55.9
Deficiency, deficient › ergosterolwith
Deficiency, deficient › ergosterol › withadult osteomalacia
M83.8
Deficiency, deficient › ergosterol › withrickets
See: Rickets
Deficiency, deficientessential fatty acid(EFA)
E63.0
Deficiency, deficienteye movements
Deficiency, deficient › eye movementssaccadic
H55.81
Deficiency, deficient › eye movementssmooth pursuit
H55.82
Deficiency, deficientfactor
See also: Deficiency, coagulation
Deficiency, deficient › factorHageman
D68.2
Deficiency, deficient › factorI(congenital) (hereditary)
D68.2
Deficiency, deficient › factorII(congenital) (hereditary)
D68.2
Deficiency, deficient › factorIX(congenital) (functional) (hereditary) (with functional defect)
D67
Deficiency, deficient › factormultiple(congenital)
D68.8
Deficiency, deficient › factor › multiple(congenital)acquired
D68.4
Deficiency, deficient › factorV(congenital) (hereditary)
D68.2
Deficiency, deficient › factorVII(congenital) (hereditary)
D68.2
Deficiency, deficient › factorVIII(congenital) (functional) (hereditary) (with functional defect)
D66
Deficiency, deficient › factor › VIII(congenital) (functional) (hereditary) (with functional defect)with vascular defect
See: Disease, von Willebrand
Deficiency, deficient › factorX(congenital) (hereditary)
D68.2
Deficiency, deficient › factorXI(congenital) (hereditary)
D68.1
Deficiency, deficient › factorXII(congenital) (hereditary)
D68.2
Deficiency, deficient › factorXIII(congenital) (hereditary)
D68.2
Deficiency, deficientfemoral, proximal focal(congenital)
See: Defect, reduction, lower limb, longitudinal, femur
Deficiency, deficientfibrin-stabilizing factor(congenital) (hereditary)
D68.2
Deficiency, deficient › fibrin-stabilizing factor(congenital) (hereditary)acquired
D68.4
Deficiency, deficientfibrinase
D68.2
Deficiency, deficientfibrinogen(congenital) (hereditary)
D68.2
Deficiency, deficient › fibrinogen(congenital) (hereditary)acquired
D65
Deficiency, deficientfolate
E53.8
Deficiency, deficientfolic acid
E53.8
Deficiency, deficientforeskin
N47.3
Deficiency, deficientfructokinase
E74.11
Deficiency, deficientfructose 1,6-diphosphatase
E74.19
Deficiency, deficientfructose-1-phosphate aldolase
E74.19
Deficiency, deficientGABA(gamma aminobutyric acid) transaminase
E72.81
Deficiency, deficientGABA-T(gamma aminobutyric acid transaminase)
E72.81
Deficiency, deficientGABA transporter 1
QA0.0131
Deficiency, deficientgalactokinase
E74.29
Deficiency, deficientgalactose-1-phosphate uridyl transferase
E74.29
Deficiency, deficientgammaglobulin in blood
D80.1
Deficiency, deficient › gammaglobulin in bloodhereditary
D80.0
Deficiency, deficientglass factor
D68.2
Deficiency, deficientglucocorticoid
E27.49
Deficiency, deficient › glucocorticoidmineralocorticoid
E27.49
Deficiency, deficientglucose-6-phosphatase
E74.01
Deficiency, deficientglucose-6-phosphate dehydrogenase
Deficiency, deficient › glucose-6-phosphate dehydrogenaseanemia
D55.0
Deficiency, deficient › glucose-6-phosphate dehydrogenasewithout anemia
D75.A
Deficiency, deficientglucose transporter protein type 1
E74.810
Deficiency, deficientglucuronyl transferase
E80.5
Deficiency, deficientGlut1
E74.810
Deficiency, deficientglycogen synthetase
E74.09
Deficiency, deficientgonadotropin(isolated)
E23.0
Deficiency, deficientgrowth hormone(idiopathic) (isolated)
E23.0
Deficiency, deficientHageman factor
D68.2
Deficiency, deficienthemoglobin
D64.9
Deficiency, deficienthepatophosphorylase
E74.09
Deficiency, deficienthomogentisate 1,2-dioxygenase
E70.29
Deficiency, deficienthormone
Deficiency, deficient › hormoneanterior pituitary(partial) NEC
E23.0
Deficiency, deficient › hormone › anterior pituitary(partial) NECgrowth
E23.0
Deficiency, deficient › hormonegrowth(isolated)
E23.0
Deficiency, deficient › hormonepituitary
E23.0
Deficiency, deficient › hormonetesticular
E29.1
Deficiency, deficienthypoxanthine-(guanine)-phosphoribosyltransferase (HG- PRT) (total H-PRT)
E79.1
Deficiency, deficientimmunity
D84.9
Deficiency, deficient › immunitycell-mediated
D84.89
Deficiency, deficient › immunity › cell-mediatedwith thrombocytopenia and eczema
D82.0
Deficiency, deficient › immunitycombined
D81.9