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Krankheitsverzeichnis

Deficiency, deficient

Krankheitsverzeichnis · Modifikatoren und Verweise

Modifikatoren und Verweise · icd10cm-index-2027.xml

Deficiency, deficient

Deficiency, deficient

3-beta hydroxysteroid dehydrogenase

E25.0

Deficiency, deficient

5-alpha reductase(with male pseudohermaphroditism)

E29.1

Deficiency, deficient

11-hydroxylase

E25.0

Deficiency, deficient

21-hydroxylase

E25.0

Deficiency, deficient

AADC(aromatic L-amino acid decarboxylase)

E70.81

Deficiency, deficient

ABCC6

Deficiency, deficient › ABCC6

causing generalized arterial calcification of infancy

E83.823

Deficiency, deficient › ABCC6

pseudoxanthoma elasticum

E83.824

Deficiency, deficient

abdominal muscle syndrome

Q79.4

Deficiency, deficient

accelerator globulin(Ac G) (blood)

D68.2

Deficiency, deficient

AC globulin(congenital) (hereditary)

D68.2

Deficiency, deficient › AC globulin(congenital) (hereditary)

acquired

D68.4

Deficiency, deficient

acid phosphatase

E83.39

Deficiency, deficient

acid sphingomyelinase(ASMD)

E75.249

Deficiency, deficient › acid sphingomyelinase(ASMD)

type

Deficiency, deficient › acid sphingomyelinase(ASMD) › type

A

E75.240

Deficiency, deficient › acid sphingomyelinase(ASMD) › type

A/B

E75.244

Deficiency, deficient › acid sphingomyelinase(ASMD) › type

B

E75.241

Deficiency, deficient

activating factor(blood)

D68.2

Deficiency, deficient

ADA2(adenosine deaminase 2)

D81.32

Deficiency, deficient

adenosine deaminase(ADA)

D81.30

Deficiency, deficient › adenosine deaminase(ADA)

with severe combined immunodeficiency(SCID)

D81.31

Deficiency, deficient › adenosine deaminase(ADA)

partial(type 1)

D81.39

Deficiency, deficient › adenosine deaminase(ADA)

specified NEC

D81.39

Deficiency, deficient › adenosine deaminase(ADA)

type 1(without SCID) (without severe combined immunodeficiency)

D81.39

Deficiency, deficient › adenosine deaminase(ADA)

type 2

D81.32

Deficiency, deficient

aldolase(hereditary)

E74.19

Deficiency, deficient

alpha-1-antitrypsin

E88.01

Deficiency, deficient

amino-acids

E72.9

Deficiency, deficient

anemia

See: Anemia

Deficiency, deficient

aneurin

E51.9

Deficiency, deficient

antibody with

Deficiency, deficient › antibody with

hyperimmunoglobulinemia

D80.6

Deficiency, deficient › antibody with

near-normal immunoglobins

D80.6

Deficiency, deficient

antidiuretic hormone

E23.2

Deficiency, deficient

anti-hemophilic

Deficiency, deficient › anti-hemophilic

factor(A)

D66

Deficiency, deficient › anti-hemophilic › factor(A)

B

D67

Deficiency, deficient › anti-hemophilic › factor(A)

C

D68.1

Deficiency, deficient › anti-hemophilic

globulin(AHG) NEC

D66

Deficiency, deficient

antithrombin(antithrombin III)

D68.59

Deficiency, deficient

aromatic L-amino acid decarboxylase(AADC)

E70.81

Deficiency, deficient

ascorbic acid

E54

Deficiency, deficient

attention(disorder) (syndrome)

F98.8

Deficiency, deficient › attention(disorder) (syndrome)

with hyperactivity

See: Disorder, attention-deficit hyperactivity

Deficiency, deficient

autoprothrombin

Deficiency, deficient › autoprothrombin

I

D68.2

Deficiency, deficient › autoprothrombin

II

D67

Deficiency, deficient › autoprothrombin

C

D68.2

Deficiency, deficient

beta-glucuronidase

E76.29

Deficiency, deficient

biotin

E53.8

Deficiency, deficient

biotin-dependent carboxylase

D81.819

Deficiency, deficient

biotinidase

D81.810

Deficiency, deficient

brancher enzyme(amylopectinosis)

E74.03

Deficiency, deficient

calciferol

E55.9

Deficiency, deficient › calciferol

with

Deficiency, deficient › calciferol › with

adult osteomalacia

M83.8

Deficiency, deficient › calciferol › with

rickets

See: Rickets

Deficiency, deficient

calcium(dietary)

E58

Deficiency, deficient

calorie, severe

E43

Deficiency, deficient › calorie, severe

with marasmus

E41

Deficiency, deficient › calorie, severe › with marasmus

and kwashiorkor

E42

Deficiency, deficient

cardiac

See: Insufficiency, myocardial

Deficiency, deficient

carnitine

E71.40

Deficiency, deficient › carnitine

due to

Deficiency, deficient › carnitine › due to

hemodialysis

E71.43

Deficiency, deficient › carnitine › due to

inborn errors of metabolism

E71.42

Deficiency, deficient › carnitine › due to

Valproic acid therapy

E71.43

Deficiency, deficient › carnitine

iatrogenic

E71.43

Deficiency, deficient › carnitine

muscle palmityltransferase

E71.314

Deficiency, deficient › carnitine

primary

E71.41

Deficiency, deficient › carnitine

secondary

E71.448

Deficiency, deficient

carotene

E50.9

Deficiency, deficient

CD73 deficiency causing arterial calcification

E83.825

Deficiency, deficient

central nervous system

G96.89

Deficiency, deficient

ceruloplasmin(Wilson)

E83.01

Deficiency, deficient

choline

E53.8

Deficiency, deficient

Christmas factor

D67

Deficiency, deficient

chromium

E61.4

Deficiency, deficient

chronic neurovisceral acid sphingomyelinase

E75.244

Deficiency, deficient

chronic visceral acid sphingomyelinase

E75.241

Deficiency, deficient

clotting(blood)

D68.9

See also: Deficiency, coagulation factor

Deficiency, deficient

clotting factor NEC(hereditary)

D68.2

See also: Deficiency, factor

Deficiency, deficient

coagulation NOS

D68.9

Deficiency, deficient › coagulation NOS

with

Deficiency, deficient › coagulation NOS › with

ectopic pregnancy

O08.1

Deficiency, deficient › coagulation NOS › with

molar pregnancy

O08.1

Deficiency, deficient › coagulation NOS

acquired(any)

D68.4

Deficiency, deficient › coagulation NOS

antepartum hemorrhage

See: Hemorrhage, antepartum, with coagulation defect

Deficiency, deficient › coagulation NOS

clotting factor NEC

D68.2

See also: Deficiency, factor

Deficiency, deficient › coagulation NOS

due to

Deficiency, deficient › coagulation NOS › due to

hyperprothrombinemia

D68.4

Deficiency, deficient › coagulation NOS › due to

liver disease

D68.4

Deficiency, deficient › coagulation NOS › due to

vitamin K deficiency

D68.4

Deficiency, deficient › coagulation NOS

newborn, transient

P61.6

Deficiency, deficient › coagulation NOS

postpartum

O72.3

Deficiency, deficient › coagulation NOS

specified NEC

D68.8

Deficiency, deficient

cognitive

F09

Deficiency, deficient

color vision

H53.50

Deficiency, deficient › color vision

achromatopsia

H53.51

Deficiency, deficient › color vision

acquired

H53.52

Deficiency, deficient › color vision

deuteranomaly

H53.53

Deficiency, deficient › color vision

protanomaly

H53.54

Deficiency, deficient › color vision

specified type NEC

H53.59

Deficiency, deficient › color vision

tritanomaly

H53.55

Deficiency, deficient

combined glucocorticoid and mineralocorticoid

E27.49

Deficiency, deficient

contact factor

D68.2

Deficiency, deficient

copper(nutritional)

E61.0

Deficiency, deficient

corticoadrenal

E27.40

Deficiency, deficient › corticoadrenal

primary

E27.1

Deficiency, deficient

craniofacial axis

Q75.009

Deficiency, deficient

cyanocobalamin

E53.8

Deficiency, deficient

C1 esterase inhibitor(C1-INH)

D84.1

Deficiency, deficient

debrancher enzyme(limit dextrinosis)

E74.03

Deficiency, deficient

dehydrogenase

Deficiency, deficient › dehydrogenase

long chain/very long chain acyl CoA

E71.310

Deficiency, deficient › dehydrogenase

medium chain acyl CoA

E71.311

Deficiency, deficient › dehydrogenase

short chain acyl CoA

E71.312

Deficiency, deficient

diet

E63.9

Deficiency, deficient

dihydropyrimidine dehydrogenase(DPD)

E88.89

Deficiency, deficient

disaccharidase

E73.9

Deficiency, deficient

edema

See: Malnutrition, severe

Deficiency, deficient

endocrine

E34.9

Deficiency, deficient

energy-supply

See: Malnutrition

Deficiency, deficient

ENPP1

Deficiency, deficient › ENPP1

causing

Deficiency, deficient › ENPP1 › causing

autosomal recessive hypophosphatemic rickets type 2

E83.822

Deficiency, deficient › ENPP1 › causing

generalized arterial calcification of infancy

E83.821

Deficiency, deficient

enzymes, circulating NEC

E88.09

Deficiency, deficient

ergosterol

E55.9

Deficiency, deficient › ergosterol

with

Deficiency, deficient › ergosterol › with

adult osteomalacia

M83.8

Deficiency, deficient › ergosterol › with

rickets

See: Rickets

Deficiency, deficient

essential fatty acid(EFA)

E63.0

Deficiency, deficient

eye movements

Deficiency, deficient › eye movements

saccadic

H55.81

Deficiency, deficient › eye movements

smooth pursuit

H55.82

Deficiency, deficient

factor

See also: Deficiency, coagulation

Deficiency, deficient › factor

Hageman

D68.2

Deficiency, deficient › factor

I(congenital) (hereditary)

D68.2

Deficiency, deficient › factor

II(congenital) (hereditary)

D68.2

Deficiency, deficient › factor

IX(congenital) (functional) (hereditary) (with functional defect)

D67

Deficiency, deficient › factor

multiple(congenital)

D68.8

Deficiency, deficient › factor › multiple(congenital)

acquired

D68.4

Deficiency, deficient › factor

V(congenital) (hereditary)

D68.2

Deficiency, deficient › factor

VII(congenital) (hereditary)

D68.2

Deficiency, deficient › factor

VIII(congenital) (functional) (hereditary) (with functional defect)

D66

Deficiency, deficient › factor › VIII(congenital) (functional) (hereditary) (with functional defect)

with vascular defect

See: Disease, von Willebrand

Deficiency, deficient › factor

X(congenital) (hereditary)

D68.2

Deficiency, deficient › factor

XI(congenital) (hereditary)

D68.1

Deficiency, deficient › factor

XII(congenital) (hereditary)

D68.2

Deficiency, deficient › factor

XIII(congenital) (hereditary)

D68.2

Deficiency, deficient

femoral, proximal focal(congenital)

See: Defect, reduction, lower limb, longitudinal, femur

Deficiency, deficient

fibrin-stabilizing factor(congenital) (hereditary)

D68.2

Deficiency, deficient › fibrin-stabilizing factor(congenital) (hereditary)

acquired

D68.4

Deficiency, deficient

fibrinase

D68.2

Deficiency, deficient

fibrinogen(congenital) (hereditary)

D68.2

Deficiency, deficient › fibrinogen(congenital) (hereditary)

acquired

D65

Deficiency, deficient

folate

E53.8

Deficiency, deficient

folic acid

E53.8

Deficiency, deficient

foreskin

N47.3

Deficiency, deficient

fructokinase

E74.11

Deficiency, deficient

fructose 1,6-diphosphatase

E74.19

Deficiency, deficient

fructose-1-phosphate aldolase

E74.19

Deficiency, deficient

GABA(gamma aminobutyric acid) transaminase

E72.81

Deficiency, deficient

GABA-T(gamma aminobutyric acid transaminase)

E72.81

Deficiency, deficient

GABA transporter 1

QA0.0131

Deficiency, deficient

galactokinase

E74.29

Deficiency, deficient

galactose-1-phosphate uridyl transferase

E74.29

Deficiency, deficient

gammaglobulin in blood

D80.1

Deficiency, deficient › gammaglobulin in blood

hereditary

D80.0

Deficiency, deficient

glass factor

D68.2

Deficiency, deficient

glucocorticoid

E27.49

Deficiency, deficient › glucocorticoid

mineralocorticoid

E27.49

Deficiency, deficient

glucose-6-phosphatase

E74.01

Deficiency, deficient

glucose-6-phosphate dehydrogenase

Deficiency, deficient › glucose-6-phosphate dehydrogenase

anemia

D55.0

Deficiency, deficient › glucose-6-phosphate dehydrogenase

without anemia

D75.A

Deficiency, deficient

glucose transporter protein type 1

E74.810

Deficiency, deficient

glucuronyl transferase

E80.5

Deficiency, deficient

glycogen synthetase

E74.09

Deficiency, deficient

gonadotropin(isolated)

E23.0

Deficiency, deficient

growth hormone(idiopathic) (isolated)

E23.0

Deficiency, deficient

Hageman factor

D68.2

Deficiency, deficient

hemoglobin

D64.9

Deficiency, deficient

hepatophosphorylase

E74.09

Deficiency, deficient

homogentisate 1,2-dioxygenase

E70.29

Deficiency, deficient

hormone

Deficiency, deficient › hormone

anterior pituitary(partial) NEC

E23.0

Deficiency, deficient › hormone › anterior pituitary(partial) NEC

growth

E23.0

Deficiency, deficient › hormone

growth(isolated)

E23.0

Deficiency, deficient › hormone

pituitary

E23.0

Deficiency, deficient › hormone

testicular

E29.1

Deficiency, deficient

hypoxanthine-(guanine)-phosphoribosyltransferase (HG- PRT) (total H-PRT)

E79.1

Deficiency, deficient

immunity

D84.9

Deficiency, deficient › immunity

cell-mediated

D84.89

Deficiency, deficient › immunity › cell-mediated

with thrombocytopenia and eczema

D82.0

Deficiency, deficient › immunity

combined

D81.9